A 46-year-old man was initially suspected of having Ménière's disease based on his clinical manifestations. The dizziness was characterized as spinning or whirling vertigo, accompanied by aural fullness and tinnitus of the right ear. Vestibular examinations were performed, including videonystagmography, vestibular evoked myogenic potential, electrocochleography, and the video head impulse test, and the central lesion was explored using magnetic resonance imaging (MRI). Vestibular examinations showed spontaneous nystagmus on the right, but the caloric and video head impulse tests were normal. Electrocochleography showed a right-side abnormality. On the third day of treatment, visual symptoms and papilledema, indicating increased intracranial pressure, were observed. Brain MRI showed cerebral venous sinus thrombosis. In conclusion, the diagnosis of Ménière's disease requires a more careful approach, and neurological signs and clinical manifestations should be checked to rule out central lesions.